Diagnostic Radiology/Musculoskeletal Imaging/Tumors Basic/Maffuci syndrome< Diagnostic Radiology | Musculoskeletal Imaging | Tumors Basic
Maffucci's syndrome is defined as multiple enchondromatosis with soft tissue and visceral hemangiomas. Patients with Maffucci's syndrome are believed to be at far greater risk for malignant transformation than those with Ollier's disease.
Fig. 1 Maffucci's syndrome. Soft tissue masses with phleboliths are consistent with hemangiomas. Note remodeling of underlying bone.
Enchondromas and Related Disorders by Jeffrey P. Kanne, M.D., University of Washington Department of Radiology